The defect in Hurler's and Hunter's syndromes: faulty degradation of mucopolysaccharide.
AUTOR(ES)
Fratantoni, J C
ACESSO AO ARTIGO
http://www.pubmedcentral.nih.gov/articlerender.fcgi?artid=225102Documentos Relacionados
- Induced Degradation of Glycosaminoglycans in Hurler's and Hunter's Syndromes by Plasma Infusion
- THE DEFECT IN HURLER AND HUNTER SYNDROMES, II. DEFICIENCY OF SPECIFIC FACTORS INVOLVED IN MUCOPOLYSACCHARIDE DEGRADATION
- The Defect in the Hurler and Scheie Syndromes: Deficiency of α-L-Iduronidase
- Acute myelogenous leukaemia in Hurler's syndrome.
- Hurler's syndrome: biosynthesis of acid mucopolysaccharides in tissue culture.